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Medical Aspect of the Aortic Diseases: the Follow-Up and Its Warnings

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6.7 Conclusion

Marfan syndrome is a genetic disease, the best recognised aetiology of ascending aortic aneurysm. Because of its genetic nature, familial screening is crucial to diagnose the disease before complications have occurred. Regular follow-up with echocardiography should allow timely surgery for aortic root replacement, ideally using a valve-sparing procedure. Beta-blockage and avoidance of violent sports are the mainstay of medical therapy and may delay surgery or even avoid it in some patients. Medical therapy and close follow-up should be maintained after surgery in all patients. Blood pressure control and close follow-up is of upmost importance in patients with persistent dissection of the descending thoracic aorta.

Patients with aortic aneurysm or dissection who do not fulfil the Marfan criteria and who have unknown aetiology, should also have systematic familial screening because of the familial pattern of inheritance in some cases.

Keywords

  • Medical Therapy
  • Aortic Aneurysm
  • Blood Pressure Control
  • Thoracic Aorta
  • Aortic Root

These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Jondeau, G., Delorme, G., Milleron, O., Wilson, J. (2006). Medical Aspect of the Aortic Diseases: the Follow-Up and Its Warnings. In: Rousseau, H., Verhoye, JP., Heautot, JF. (eds) Thoracic Aortic Diseases. Springer, Berlin, Heidelberg . https://doi.org/10.1007/3-540-38309-3_6

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