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Churg–Strauss Syndrome

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Systemic Vasculitis

Part of the book series: Medical Radiology ((Med Radiol Diagn Imaging))

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Abstract

Churg–Strauss syndrome is a rare diffuse vasculitis that is closely associated with a severe asthma. The clinical diagnosis may be difficult in the early stages. Nevertheless, the onset of severe asthma in an adult and the emergence of extrarespiratory manifestations should alert one to the probable diagnosis of Churg–Strauss syndrome. Imaging is useful to assess the cardiorespiratory system and the sinus cavities. Pathological confirmation can be challenging as the characteristic histological features are often incomplete. Prognosis is usually good with corticosteroid therapy alone or in combination with immunosuppressive drugs.

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Authors and Affiliations

  1. Department of Medical Imaging, Medical School of Tunis, Interior Security Forces Teaching Hospital, 2070, La Marsa, Tunisia

    M. Habib Bouhaouala & Mehdi Charfi

  2. Department of Internal Medicine, Medical School of Tunis, Mongi Slim University Hospital, 2046, La Marsa, Sidi Daoud, Tunisia

    Kamel Bouslama

  3. Department of Pneumology, Medical School of Tunis, La Rabta University Hospital, 1007, Tunis Jabbari, Tunisia

    Nadia Mhiri & Majed El Beji

  4. Department of Imaging, Centre Hospitalier Intercommunal des Portes de l’Oise, Creteil, France

    M. Habib Ben Romdhane

  5. Department of Medical Imaging and Imaging Guided Interventions, Mongi Slim University Hospital, 2046, La Marsa, Sidi Daoud, Tunisia

    Lotfi Hendaoui

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  1. M. Habib Bouhaouala
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  2. Kamel Bouslama
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  3. Mehdi Charfi
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  4. Nadia Mhiri
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  5. M. Habib Ben Romdhane
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  7. Lotfi Hendaoui
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Correspondence to M. Habib Bouhaouala .

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Editors and Affiliations

  1. Medical School of Tunis, Department of Medical Imaging, Hôpital Mongi Slim, La Marsa, 2046, Tunisia

    Lotfi Hendaoui

  2. Mayo Graduate School of Medicine, Gonda Vascular Center, Mayo Clinic, Rochester, 55902, Minnesota, USA

    Anthony W. Stanson

  3. Medical School of Tunis, Department of Medical Imaging, Interior Security Forces Teaching Hospit, La Marsa, 2070, Tunisia

    M. Habib Bouhaouala

  4. Medical School of Toulouse University, Department of Medical Imaging, Rangueil Hospital, Toulouse CX 9, 31059, France

    Francis Joffre

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Bouhaouala, M.H. et al. (2011). Churg–Strauss Syndrome. In: Hendaoui, L., Stanson, A., Bouhaouala, M., Joffre, F. (eds) Systemic Vasculitis. Medical Radiology(). Springer, Berlin, Heidelberg. https://doi.org/10.1007/174_2011_291

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  • DOI: https://doi.org/10.1007/174_2011_291

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