Ophthalmic Vasculitis

  • M. Habib Bouhaouala
  • Lamia El Fekih
  • Mehdi Charfi
  • Lotfi Hendaoui
Part of the Medical Radiology book series (MEDRAD)


Orbital involvement in systemic vasculitis is common especially during the granulomatous vasculitis associated with antineutrophil cytoplasmic antibodies (ANCA) and Behçet diesease. Ophthalmic manifestations are in connection with extra- or intraocular blood vessel involvement. Ophthalmic evaluation with a fundus oculi examination, laboratory tests and chest X-ray are systematic. Orbital, facial, and cerebral imaging (CT and MRI) studies may be useful to assess the diagnosis.


Rheumatic Disease Systemic Vasculitis Antineutrophil Cytoplasmic Antibody Complete Blood Cell Count Vessel Involvement 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


  1. Abitbol O (2003) Maladie de Eales. EMC (Elsevier Masson SAS, Paris), Ophtalmologie 21-230-B-05Google Scholar
  2. Andm M, Schmidt J, Chanet V, Aumaitre O (1998) Ophtalmoplégie douloureuse au cours d’un syndrome de Churg et Strauss. Rev Med Interne 19(suppl 1):136sGoogle Scholar
  3. Chakravarty K (1997) Vasculitis by organ systems. Baillieres Clin Rheum 2:357–393CrossRefGoogle Scholar
  4. Delarbre X, André M, Dalens H et al (2001) Manifestations ophtalmologiques des vascularites systémiques: analyse de six observations et revue de la littérature. Rev Med Interne 22:1039–1048PubMedCrossRefGoogle Scholar
  5. Gaundong Mbéthé GL, Diéval C, Lafitte A, Roger-Schmeltz J, Longy-Boursier M, Mercié P (2010) Wegener’s granulomatosis with anti-MPO c-ANCA revealed by uveitis. Rev Med Interne 31:e11–e13CrossRefGoogle Scholar
  6. Guillevin L, Pagnoux C (2006) Principales vascularites nécrosantes systémiques. EMC (Elsevier Masson SAS, Paris), Appareil locomoteur, 14-245-F-10Google Scholar
  7. Hajji Z, Berraho A (2003) Oeil et maladie de Behçet. EMC (Elsevier Masson SAS, Paris), Ophtalmologie, 21-225-C-20Google Scholar
  8. Jayne D (2009) The diagnosis of vasculitis. Best Pract Res Clin Rheum 23:445–453CrossRefGoogle Scholar
  9. Khasnis A, Langford CA (2009) Update on vasculitis. J Allergy Clin Immunol 123:1226–1236PubMedCrossRefGoogle Scholar
  10. Lutt JR, Lim LL, Phal PM, Rosenbaum JT (2008) Orbital inflammatory disease. Sem Arthritis Rheum 37:207–222CrossRefGoogle Scholar
  11. Mafee ME, Valvassori GE, Becker M (2005) Vasculitides. In: Lewin JS, Nour SG, Weber AL (eds.) Imaging of the head and neck, 2nd edn. Georg Thieme Verlag, Stuttgart, New YorkGoogle Scholar
  12. Mili-Boussen I, Letaief I, Zbiba W (2010) Retinal vasculitis. Epidemiological, clinical and etiological features. J Fr Ophtalmol 33:529–537PubMedCrossRefGoogle Scholar
  13. Montagnac R, Nyandwi J, Loiselet G, Pradel J, Schillinger F (2009) Ophthalmic manifestations in Wegener’s granulomatosis—review of literature about an observation. Nephrol Ther 5:603–613PubMedGoogle Scholar
  14. Perez VL, Chavala SH, Ahmed M (2004) Ocular manifestations and concepts of systemic vasculitides. Surg Ophthalmol 49:399–418CrossRefGoogle Scholar
  15. Puechal X (2007) Vascularites associées aux anticorps anticytoplasme des polynucléaires. Rev Rhum 74:824–832CrossRefGoogle Scholar
  16. Silvera S, Vignaux O, Legman P (2007) Imagerie de l’atteinte ORL et cérébrale de la maladie de Wegener. Presse Med 36:913–921PubMedCrossRefGoogle Scholar
  17. Takanashi T, Uchida S, Arita M, Okada M, Kashii S (2001) Orbital inflammatory pseudotumor and ischemic vasculitis in Churg-Strauss syndrome—report of two cases and review of the literature. Ophthalmology 108:1129–1133PubMedCrossRefGoogle Scholar
  18. Wechsler B, Du-Boutin LTH, Amoura Z (2009) Maladie de Behçet. EMC (Elsevier Masson SAS, Paris), Appareil locomoteur, 14-206-B-10Google Scholar

Copyright information

© Springer-Verlag Berlin Heidelberg 2011

Authors and Affiliations

  • M. Habib Bouhaouala
    • 1
  • Lamia El Fekih
    • 2
  • Mehdi Charfi
    • 1
  • Lotfi Hendaoui
    • 3
  1. 1.Department of Medical ImagingMedical School of Tunis, Interior Security Forces Teaching HospitalLa MarsaTunisia
  2. 2.Department of OphtalomologyMedical School of Tunis, Internal Security Forces HospitalLa MarsaTunisia
  3. 3.Department of Medical ImagingMedical School of Tunis, Mongi Slim University HospitalLa MarsaTunisia

Personalised recommendations