Imaging of Kawasaki Disease
Kawasaki disease (KD) is an acute systemic disease with generalized vasculitis with unknown etiology that occurs predominantly in infants and young children. The most feared complication is myocardial infarction and death due to thrombosis of coronary artery aneurysms. Imaging plays an important role in early diagnosis and follow up of the disease. Echocardiography is rapidly accessible and innocuous, and it is the modality of choice for the initial diagnosis and follow-up of coronary artery lesions in young patients with KD. MDCT coronary angiography is more sensitive than echocardiography for the detection of aneurysms located on the distal segments. Radiation exposure in children is still a main limitation to the use of this technique for the follow-up of the disease. MRI is an interesting noninvasive technique for the evaluation of coronary arteries, myocardial perfusion and left ventricular function. Coronary angiography is still the gold standard for coronary artery lumen evaluation but remains invasive and is mainly reserved for cases where catheter interventions should be performed.
KeywordsCoronary Artery Kawasaki Disease Coronary Artery Stenosis Coronary Artery Aneurysm Coronary Artery Lesion
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