Liver Transplantation for Budd–Chiari Syndrome

  • Yasuhiko SugawaraEmail author
  • Taizo Hibi


Liver transplantation is indicated for rapidly progressing Budd–Chiari syndrome (BCS) after failure of conventional treatment. Outflow reconstruction is key in BCS cases. The area of the venous outflow obstruction varies among cases. The hepatic veins of the liver graft must be anastomosed with a patent outflow tract of the recipient. After transplantation, the 5-year survival rate of patients with BCS is approximately 75%. As patients with BCS are often in a prothrombotic state, long-term anticoagulation therapy should be maintained after liver transplantation.


Anticoagulation Hepatic vein thrombosis Transjugular intrahepatic portosystemic shunt 



Budd–Chiari syndrome


Transjugular intrahepatic portosystemic shunt


Hepatic veins


Inferior vena cava


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© Springer Nature Singapore Pte Ltd. 2020

Authors and Affiliations

  1. 1.Department of Transplantation/Pediatric SurgeryPostgraduate School of Life Science, Kumamoto UniversityKumamotoJapan

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