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Liver Transplantation for Budd–Chiari Syndrome

  • Yasuhiko SugawaraEmail author
  • Taizo Hibi
Chapter

Abstract

Liver transplantation is indicated for rapidly progressing Budd–Chiari syndrome (BCS) after failure of conventional treatment. Outflow reconstruction is key in BCS cases. The area of the venous outflow obstruction varies among cases. The hepatic veins of the liver graft must be anastomosed with a patent outflow tract of the recipient. After transplantation, the 5-year survival rate of patients with BCS is approximately 75%. As patients with BCS are often in a prothrombotic state, long-term anticoagulation therapy should be maintained after liver transplantation.

Keywords

Anticoagulation Hepatic vein thrombosis Transjugular intrahepatic portosystemic shunt 

Abbreviations

BCS

Budd–Chiari syndrome

TIPS

Transjugular intrahepatic portosystemic shunt

HV

Hepatic veins

IVC

Inferior vena cava

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Copyright information

© Springer Nature Singapore Pte Ltd. 2020

Authors and Affiliations

  1. 1.Department of Transplantation/Pediatric SurgeryPostgraduate School of Life Science, Kumamoto UniversityKumamotoJapan

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