Functional Single Ventricle (FSV)

  • In Sook Park
  • Hyun Woo Goo


This chapter includes classification, morphology, clinical manifestations, diagnosis, natural and unnatural course, treatment, staged Fontan operation, and fetal diagnosis of a functional single ventricle. Particularly, the chapter includes a unique and novel classification of a functional single ventricle, which can be applied to every heart that requires Fontan-type operation. Images of real patients of each type are presented. Also various postoperative problems or sequelae after bidirectional cavopulmonary shunt and Fontan operation and their treatment are presented including images of each problem.


Univentricular heart Double-inlet ventricle Holmes’ heart Rudimentary chamber Fontan operation Bidirectional cavopulmonary shunt Systematic approach Damus–Kaye–Stansel operation Stent implantation Pulmonary A-V malformation Anticoagulation Protein-losing enteropathy Plastic bronchitis Liver fibrosis Pregnancy Heart transplantation 

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Copyright information

© Springer Nature Singapore Pte Ltd. 2019

Authors and Affiliations

  • In Sook Park
    • 1
  • Hyun Woo Goo
    • 2
  1. 1.Department of Pediatric CardiologyUniversity of Ulsan College of Medicine, Asan Medical CenterSeoulSouth Korea
  2. 2.Department of RadiologyUniversity of Ulsan College of Medicine, Asan Medical CenterSeoulSouth Korea

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