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Alveolar Soft Part Sarcoma

  • Mariel Angelou Parulan
  • Shantha AmrithEmail author
  • Stephanie Ming Young
  • Eric Ting
  • Bingcheng Wu
  • Min En Nga
  • Gangadhara Sundar
Chapter

Abstract

Alveolar soft part sarcoma (ASPS) is a rare malignancy that accounts for less than 1% of all soft tissue tumours. In a localized disease, it has a reported 5-year disease-free survival of 71% and decreases to 20% in patients who present with metastases. Although it has been more than half a decade since this condition has been reported, there is still limited knowledge available regarding this condition. Since this may present similar to other types of soft tissue tumours in the orbit, histologic evaluation becomes vital. Local surgical excision appears to provide the best chance of controlling the disease involving the orbit.

Further Reading

  1. 1.
    Chung EM, Smirniotopoulos JG, Specht CS, Schroeder JW, Cube R. From the archives of the AFIP: pediatric orbit tumours and tumour like lesions: non-osseous lesions of the extraocular orbit. Radiographics. 2007;27(6):1777–99.CrossRefPubMedGoogle Scholar
  2. 2.
    Fay A, Dolman PJ. Diseases and disorders of the orbit and ocular adnexa. Edinburgh: Elsevier; 2017.Google Scholar
  3. 3.
    Folpe AL, Deyrup AT. Alveolar soft-part sarcoma: a review and update. J Clin Pathol. 2006;59(11):1127–32.CrossRefPubMedPubMedCentralGoogle Scholar
  4. 4.
    Honavar S, Reddy VA, Mulay K, Ali M. Orbital alveolar soft-part sarcoma: clinico-pathological profiles, management and outcomes. J Cancer Res Ther. 2014;10(2):294.CrossRefPubMedGoogle Scholar
  5. 5.
    Rose AM, Kabiru J, Rose GE. Alveolar soft-part sarcoma of the orbit. Afr J Paediatr Surg. 2011;8(1):82–4.CrossRefPubMedGoogle Scholar

Copyright information

© Springer Nature Singapore Pte Ltd. 2019

Authors and Affiliations

  • Mariel Angelou Parulan
    • 1
  • Shantha Amrith
    • 1
    • 2
    Email author
  • Stephanie Ming Young
    • 1
    • 2
  • Eric Ting
    • 3
    • 4
    • 5
  • Bingcheng Wu
    • 6
  • Min En Nga
    • 6
    • 7
  • Gangadhara Sundar
    • 1
    • 2
  1. 1.Department of OphthalmologyNational University HospitalSingaporeSingapore
  2. 2.Department of OphthalmologyYong Loo Lin School of Medicine, National University of SingaporeSingaporeSingapore
  3. 3.Department of Diagnostic ImagingNational University HospitalSingaporeSingapore
  4. 4.Department of Diagnostic ImagingYong Loo Lin School of Medicine, National University of SingaporeSingaporeSingapore
  5. 5.Advanced Medicine ImagingSingaporeSingapore
  6. 6.Department of PathologyNational University HospitalSingaporeSingapore
  7. 7.Department of PathologyYong Loo Lin School of Medicine, National University of SingaporeSingaporeSingapore

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