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Tumors and Related Lesions of the Retinal Pigmented Epithelium

  • Carol L. Shields
  • Jerry A. Shields
Chapter
Part of the Retina Atlas book series (RA)

Abstract

There are a variety of pigment epithelial tumors, including benign and malignant types. Some are considered congenital such as congenital hypertrophy of the retinal pigment epithelium (CHRPE) (solitary and multifocal), congenital simple hamartoma, and torpedo maculopathy. Some are presumed acquired such as adenoma and adenoma of the pigment epithelium. These lesions can clinically simulate malignant tumors, particularly malignant melanoma of the iris, ciliary body, and choroid (Shields and Shields 2015; Shields and Shields 2017a, b, c).

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Copyright information

© Springer Nature Singapore Pte Ltd. 2019

Authors and Affiliations

  • Carol L. Shields
    • 1
    • 2
  • Jerry A. Shields
    • 1
    • 2
  1. 1.Ocular Oncology ServiceWills Eye HospitalPhiladelphiaUSA
  2. 2.Department of OphthalmologyThomas Jefferson UnversityPhiladelphiaUSA

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