Pathology of Non-cirrhotic Liver Disease
The pathology of non-cirrhotic liver diseases causing portal hypertension such as extrahepatic portal obstruction, idiopathic portal hypertension, nodular regenerative hyperplasia, veno-occlusive disease, and Budd-Chiari syndrome is mainly explained.
The interrupted region of the portal circulation and hepatic blood flow pattern vary depending on disease, and several factors are combined in the mechanism of portal pressure elevation in many cases. Accordingly, the pathology varies among diseases and cases, showing diversity. Understanding the pathology of the liver and vascular system in patients with non-cirrhotic liver diseases causing portal hypertension is important to accurately clarify the diverse pathology of those diseases and useful in making a diagnosis and prognosis.
KeywordsPortal hypertension Liver pathology Extrahepatic portal obstruction (EHO) Idiopathic portal hypertension (IPH) Budd-Chiari syndrome (BCS)
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