Imaging: ERCP

  • Atsushi KannoEmail author
  • Atsushi Masamune
  • Tooru Shimosegawa


Further insights into autoimmune pancreatitis (AIP) have been revealed by many researchers since a report by Yoshida et al. in 1995 [1]. Bile duct stricture accompanied by AIP has been considered as IgG4-related sclerosing cholangitis (IgG4-SC) based on several reports [2, 3]. Recently, IgG4-SC is regarded as a manifestation of a systemic IgG4-related disease (IgG4-RD) [4]. The diagnosis of IgG4-SC is based on the clinical diagnostic criteria of IgG4-related sclerosing cholangitis 2012 [5]. The clinical symptoms of IgG4-SC are similar to those of AIP. IgG4-SC is often observed in patients aged 60 years or older; it is more common in males, is associated with elevated levels of serum IgG4, and responds well to steroids. A progressive course, such as that observed in cases of primary sclerosing cholangitis (PSC), is rare, and the short-term prognosis is extremely favorable. However, the long-term prognosis for IgG4-SC remains unclear. Accurate diagnosis of IgG4-SC is essential for proper management of this disease. We present bile duct images using endoscopic retrograde cholangiopancreatography (ERCP) in cases of IgG4-SC.


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Copyright information

© Springer Science+Business Media Singapore 2019

Authors and Affiliations

  • Atsushi Kanno
    • 1
    Email author
  • Atsushi Masamune
    • 1
  • Tooru Shimosegawa
    • 1
  1. 1.Division of GastroenterologyTohoku University Graduate School of MedicineSendaiJapan

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