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Jejunal Motility in Dystrophia Myotonica: a Manometric Study of Migrating Motor Complex

  • D. Couturier
  • S. Grandjouan
  • L. Elouaer-Blanc
  • A. Verduron
  • B. Travers
  • J. C. Turpin
  • R. Bouche
  • J. Guerre

Abstract

Dystrophia Myotonica (DM) is a hereditary disease characterized mainly by progressive muscular atrophy and myotonia involving skeletal muscles with progressive muscle wasting and weakness. The electrophysiological feature of the disease is repetitive discharges of striated muscle cell membrane observed after voluntary or induced contractions. Cataract, testiculus atrophy, mental deficiency and fronto-parietal baldness are the more commun extramuscular symptoms of the disease (1, 2, 3). Cardiac muscle is commonly involved and conduction defects are observed. Gastrointestinal smooth muscle may also be involved : oesophagus (4, 5), stomach (6, 7), colon (8) and anal sphincter (9).

Keywords

Gastrointestinal Motility Myotonic Dystrophy Proximal Jejunum Migrate Motor Complex Intestinal Pseudo Obstruction 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© MTP Press Limited 1984

Authors and Affiliations

  • D. Couturier
  • S. Grandjouan
  • L. Elouaer-Blanc
  • A. Verduron
  • B. Travers
  • J. C. Turpin
  • R. Bouche
  • J. Guerre

There are no affiliations available

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