Disorders of Cerebrospinal Fluid Circulation

Chapter

Abstract

Spontaneous intracranial hypotension (SIH) and idiopathic intracranial hypertension (IIH) are rare and have uncertain pathogenesis. Idiopathic normal pressure hydrocephalus (iNPH) is a more frequent disease in which specific characteristics predict therapeutic response.

SIH: Most patients obtain complete recovery by conservative management. Epidural blood patch is quite often efficacious; surgery is reserved for refractory cases. Rare patients remain symptomatic and work disabled.

IIH is a chronic disease requiring long-term treatment. Permanent, mild, or moderate/severe visual field defects are reported.

iNPH: Ventricular-peritoneal shunting remains the preferred treatment of the disorder. The overall success rate is 30–96 %.

Keywords

Idiopathic intracranial hypertension Pseudotumor cerebri syndrome Spontaneous intracranial hypotension Normal pressure hydrocephalus 
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Copyright information

© Springer-Verlag Italia 2015

Authors and Affiliations

  1. 1.Neuroradiology DepartmentIRCCS Foundation Istituto Neurologico Carlo BestaMilanItaly

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