IgG4-Related Kidney Disease: Pathological Features: Other Glomerular Disease

  • Satoshi HisanoEmail author


IgG4-related disease (IgG4-RD) is a recently-recognized systemic disease that often affects the kidneys. Although the most common renal lesion in IgG4-RD is tubulointerstitial nephritis, a variety of glomerular lesions associated with IgG4-related kidney disease (IgG4-RKD) have also been reported. Membranous glomerulonephritis is the most common glomerular finding. Other associated glomerular diseases include mesangial proliferative glomerulonephritis, IgA nephropathy, Henoch-Schönlein pupura nephritis (IgA vasculitis), membranoproliferative glomerulonephritis, endocapillary proliferative glomerulonephritis and minimal change disease. Some of the less common glomerular conditions associated with IgG4-RKD are discussed in this chapter.


IgG4-related kidney disease IgA vasculitis Membranoproliferative glomerulonephritis Th2 cell Treg cell 


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Copyright information

© Springer Japan 2016

Authors and Affiliations

  1. 1.Department of Pathology, Faculty of MedicineFukuoka UniversityFukuokaJapan

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