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Zusammenfassung

Verschiebungen des Größenverhältnisses zwischen Herz und Lungen sowie die Verlagerung von Herz und Mediastinum sind häufig Ausdruck einer intrathorakalen Pathologie oder eines Zwerchfelldefekts. Zu den häufigsten Lungenfehlbildungen gehören bronchopulmonale Anomalien (z. B. CCAML), vaskuläre Anomalien und kombinierte Anomalien von Lunge und Gefäßsystem (z. B. Sequestration). Thorakale Anomalien können zu einer Lungenhypoplasie und damit zu einer erhöhten postnatalen Morbidität und Mortalität führen. Die häufigste intrathorakale Ursache der Lungenhypoplasie ist die fetale Zwerchfellhernie, andere intrathorakale Ursachen sind ein ausgeprägter Hydrothorax, die CCAML oder ein Lungensequester. Die Entbindung von Kindern mit diesen Krankheitsbildern sollte immer am Perinatalzentrum erfolgen, da viele der Neugeborenen symptomatisch sind und eine entsprechende neonatologische Intensivtherapie bis hin zur sofortigen kinderchirurgischen Intervention benötigen.

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Copyright information

© Springer-Verlag GmbH Deutschland 2018

Authors and Affiliations

  1. 1.Universitätsklinikum BonnAbt. für Geburtshilfe/Pränatale MedizinBonnDeutschland
  2. 2.Universitätsklinikum Hamburg-EppendorfKlinik und Poliklinik für GeburtshilfeHamburgDeutschland

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