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Kapilläre Nävi und andere vaskuläre Malformationen

  • Rudolf Happle
Chapter
Part of the Springer Reference Medizin book series (SRM)

Zusammenfassung

Die Bezeichnung kapilläre Malformation hat auf internationaler Ebene Verwirrung gestiftet. Die hier vorgeschlagene Klassifikation befolgt das Prinzip, dass jeder spezifischen Hautkrankheit ein spezifischer Name zukommt. Kapilläre Nävi sind Naevus flammeus, Portweinnävus vom Proteus-Typ, Portweinnävus vom CLOVES-Typ, Naevus roseus, rhodoider Nävus, Cutis marmorata teleangiectatica congenita, Livedo reticularis congenita, segmentales Angioma serpiginosum, Naevus anaemicus, Naevus syringocapillaris, Naevus vascularis mixtus und Angiokeratoma circumscriptum. Weitere mögliche kapilläre Nävi sind mesotroper Portweinfleck, Carter-Mirzaa-Flecken sowie unilaterale nävoide Teleangiektasien vom punktförmigen oder fleckförmigen Typ. Hinzu kommen der segmentale Naevus venosus und die hereditären kleinen venösen Nävi. Lymphatische Malformationen umfassen Naevus lymphangioreticularis und die lymphatische Kokardenmalformation, die bislang als Hämangiom fehlgedeutet worden ist.

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Copyright information

© Springer-Verlag GmbH Deutschland, ein Teil von Springer Nature 2018

Authors and Affiliations

  1. 1.Klinik für Dermatologie und VenerologieUniversitätsklinikum FreiburgFreiburgDeutschland

Section editors and affiliations

  • Michael Hertl
    • 1
  1. 1.Klinik für Dermatologie und Allergologie, Universitätsklinikum MarburgMarburgDeutschland

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