Neuroendocrine Tumours pp 271-274 | Cite as
Less Common Types of Pancreatic Neuroendocrine Tumors
Chapter
Abstract
Less common types of pancreatic neuroendocrine tumors (pNETs) or rare functional pNETs, which include ACTHoma, CRHoma, serotoninoma, calcitoninoma, GHRHoma, GRFoma, parathyroid hormone-related peptide tumor, and ghrelinoma, mainly occur in the pancreas but may also develop in other areas. The clinical features of rare pNETs include specific clinical syndromes associated with ectopic hormone secretion. Because the incidence is extremely low, it is often difficult to define pNETs as a distinct syndrome in most cases. The diagnosis and treatment strategies for less common pNETs are similar to those of other common pNETs.
Keywords
Tuberous Sclerosis Complex Neuroendocrine Carcinoma Pancreatic Neuroendocrine Tumor Adequate Lymph Node pNET Patient
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.
References
- 1.Jensen RT, Cadiot G, Brandi ML et al (2012) ENETS Consensus Guidelines for the management of patients with digestive neuroendocrine neoplasms: functional pancreatic endocrine tumor syndromes. Neuroendocrinology 95:98–119. doi: 10.1159/000335591 CrossRefPubMedCentralPubMedGoogle Scholar
- 2.Tsuchihashi T, Yamaguchi K, Abe K, Yanaihara N, Saito S (1992) Production of immunoreactive corticotropin-releasing hormone in various neuroendocrine tumors. Jpn J Clin Oncol 22:232–237PubMedGoogle Scholar
- 3.Berger G, Trouillas J, Bloch B et al (1984) Multihormonal carcinoid tumor of the pancreas: secreting growth hormone-releasing factor as a cause of acromegaly. Cancer 54:2097–2108CrossRefPubMedGoogle Scholar
- 4.Corbetta S, Peracchi M, Cappiello V et al (2003) Circulating ghrelin levels in patients with pancreatic and gastrointestinal neuroendocrine tumors: identification of one pancreatic ghrelinoma. J Clin Endocrinol Metab 88:3117–3120. doi: 10.1210/jc.2002-021842 CrossRefPubMedGoogle Scholar
- 5.Jensen RT, Berna MJ, Bingham DB, Norton JA (2008) Inherited pancreatic endocrine tumor syndromes: advances in molecular pathogenesis, diagnosis, management, and controversies. Cancer 113(7 suppl):1807–1843. doi: 10.1002/cncr.23648 CrossRefPubMedCentralPubMedGoogle Scholar
- 6.Öberg K (2010) Pancreatic endocrine tumors. Semin Oncol 37:594–618. doi: 10.1053/j.seminoncol.2010.10.014 CrossRefPubMedGoogle Scholar
- 7.Metz DC, Jensen RT (2008) Gastrointestinal neuroendocrine tumors: pancreatic endocrine tumors. Gastroenterology 135:1469–1492. doi: 10.1053/j.gastro.2008.05.047 CrossRefPubMedCentralPubMedGoogle Scholar
Copyright information
© Springer-Verlag Berlin Heidelberg 2015