Airway Management in Patients with Robin Sequence

  • Kevin D. Han
  • Mitchel Seruya
  • Diego A. Preciado
  • Albert K. Oh
Chapter

Abstract

Airway management in infants with Robin sequence (RS) remains controversial, ranging from conservative to operative modalities. In some centers, tracheostomy remains the mainstay for those infants with severe respiratory obstruction. We present here a retrospective review of 61 infants with RS at a large tertiary center from 1994 to 2010. Patients who had undergone tracheostomy were identified. Baseline demographics, complications, mortality, and time to decannulation without further surgical intervention (i.e., “natural” decannulation) were recorded. We witnessed that tracheostomy in infants with RS is associated with inordinately high rates of mortality and morbidity and long-term tracheostomy dependence, particularly patients with syndromic RS.

Keywords

Airway Obstruction Airway Management Orthopedic Device Mandibular Growth Robin Sequence 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

Abbreviations

CNMC

Children’s National Medical Center

CPT

Current Procedure Terminology

ICD – 9

International Classifications of ­Diseases Version 9

LOS

Length of hospital stay

NPA

Nasopharyngeal airway

RS

Robin sequence

SPSS

Statistical Program for Social Sciences

TLA

Tongue-lip adhesion

Notes

Financial Disclosure Information

The authors have no financial or commercial interests to disclose.

Conflict of Interest

None

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Copyright information

© Springer-Verlag Berlin Heidelberg 2013

Authors and Affiliations

  • Kevin D. Han
    • 1
  • Mitchel Seruya
    • 1
  • Diego A. Preciado
    • 2
    • 3
  • Albert K. Oh
    • 4
    • 5
  1. 1.Department of Plastic Surgery, 1PHCGeorgetown University HospitalWashington, DCUSA
  2. 2.Department of Otolaryngology, Pediatrics, and Integrative Systems BiologyThe George Washington University School of MedicineWashington, DCUSA
  3. 3.Division of Pediatric Otolaryngology, Department of OtolaryngologyChildren’s National Medical CenterWashington, DCUSA
  4. 4.Department of Surgery and PediatricsThe George Washington University School of MedicineWashington, DCUSA
  5. 5.Department of Plastic and Reconstructive SurgeryChildren’s National Medical CenterWashington, DCUSA

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