Degenerative Hollow Visceral Myopathy Mimicking Hirschsprung’s Disease

  • H. Rode
  • R.A. Brown
  • A. Numanoglu


Intestinal motility is a highly coordinated process and depends on smooth muscle contractility, the pacemaker activity evoked by the intestinal cells of Cajal, and the summation of the effects of the enteric and autonomic nervous systems on gut function. Crippling gastrointestinal dysfunction can result from a variety of abnormalities, involving these elements individually or in combination.


Celiac Disease Muscularis Propria Mixed Connective Tissue Disease Progressive Systemic Sclerosis Longitudinal Muscle Layer 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.


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Copyright information

© Springer-Verlag Berlin Heidelberg 2008

Authors and Affiliations

  • H. Rode
    • 1
  • R.A. Brown
    • 1
  • A. Numanoglu
    • 1
  1. 1.Department of Paediatric SurgeryRed Cross Children’s HospitalCape TownSouth Africa

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