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Megacystis-Microcolon-Intestinal Hypoperistalsis Syndrome

Abstract

Megacystis-microcolon-intestinal hypoperistalsis syndrome (MMIHS) is a rare congenital and generally fatal cause of functional intestinal obstruction in the newborn. This syndrome is characterized by abdominal distension caused by a distended nonobstructed urinary bladder, microcolon and decreased or absent intestinal peristalsis [1]. Usually incomplete intestinal rotation and shortened small bowel are associated.

Keywords

Prenatal Diagnosis Vacuolar Degeneration Neuronal Nicotinic Acetylcholine Receptor Megacystis Microcolon Intestinal Hypoperistalsis Syndrome Giant Ganglion 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer-Verlag Berlin Heidelberg 2008

Authors and Affiliations

  • P. Puri
    • 1
  1. 1.Children’s Research Centre, Our Lady’s Children’s HospitalUniversity College of DublinCrumlinIreland

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