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Acute Exacerbation of Idiopathic Pulmonary Fibrosis

  • Joyce S. LeeEmail author
  • Harold R. Collard
Chapter
Part of the Respiratory Medicine book series (RM)

Abstract

Acute exacerbation (AEx) of idiopathic pulmonary fibrosis (IPF) is a clinically important complication of IPF that carries a high morbidity and mortality. In the last decade we have learned much about this event, but there are many remaining questions: What is it? Why does it happen? How can we prevent it? How can we treat it? This chapter attempts to summarize and update our current understanding of the epidemiology, etiology, and management of acute exacerbation of IPF and point out areas where additional data are needed.

Keywords

Acute exacerbation Risk factors Pathobiology Diagnosis Prognosis Management 

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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  1. 1.Department of Medicine, Division of Pulmonary Sciences and Critical Care MedicineUniversity of Colorado Denver – Anschutz Medical CampusAuroraUSA
  2. 2.Department of MedicineUniversity of California San FranciscoSan FranciscoUSA

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