Relapsing Polychondritis

  • M. B. Adarsh
  • Aman Sharma
Part of the Rare Rheumatic Diseases book series (RRD)


Relapsing polychondritis (RP) is a rare chronic autoimmune disease of unknown etiology. The disease is characterized by episodic inflammation of cartilaginous structures affecting hyaline, elastic and fibro cartilages. Proteoglycan-rich organs such as the eye, heart, blood vessels, and inner ear are also affected. It was first described in the literature in 1923 by Austrian physician Von jaksch-Wartenorst. Polychondropathia was the term initially used to describe this entity. Current nomenclature of relapsing polychondritis was proposed in 1960 by Pearson et al. RP is known to be associated with a number of rheumatologic conditions including vasculitis, rheumatoid arthritis, and systemic lupus erythematosus (SLE).


Relapsing polychondritis Autoimmune disease RP Cartilage inflammation 


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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  • M. B. Adarsh
    • 1
  • Aman Sharma
    • 1
  1. 1.Department of Internal MedicinePostgraduate Institute of Medical Education and ResearchChandigarhIndia

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