Juvenile Dermatomyositis in Adolescents and Young Adults
Juvenile dermatomyositis (JDM) is a rare disease but the most common idiopathic inflammatory myopathy (IIM) of childhood. It is a systemic vasculopathy primarily affecting the skin and muscles, causing classic signs of rash and proximal muscle weakness, but can present with heterogeneous features, natural history and outcomes. This chapter highlights the differences between paediatric and adult disease in clinical presentation and presents an update of treatment strategies and outcomes of the disease including cardiovascular involvement, reproductive health and vocational developmental milestones.
KeywordsJuvenile dermatomyositis Cardiovascular involvement Long-term outcomes Calcinosis
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