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Congenital Pulmonary Airway Malformations: From the Prenatal Diagnosis to the Postoperative Follow-Up

  • Arnaud BonnardEmail author
Chapter

Abstract

Since a couple of years now, several things evolved and changed for congenital pulmonary airway malformations (CPAM). From the understanding of the malformation to the prenatal diagnosis and the rising place of the minimally invasive surgery, CPAM became a subject of interest for all pediatric surgeons all over the world. Most of the recent publications are related to the surgery itself and the growing place of minimal invasive surgery helped by new instruments pushing further the indications. This does not have to hide the recent progresses made in the comprehension of the pathology of these malformations and especially the closed relations between CPAM and pleuropulmonary blastoma (PPB). In the first part, we will talk about the classification and the pathology of these malformations. Then, we will move to the prenatal diagnosis and specifically the prenatal procedures sometimes required in the severe form of CPAM. At last, we will treat of the surgery and the follow-up.

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Copyright information

© Springer Nature Switzerland AG 2019

Authors and Affiliations

  1. 1.Department of General Pediatric SurgeryRobert Debre Children University Hospital, APHPParisFrance

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