Acute Heart Failure in Adult Patients with Congenital Heart Disease

  • Alexander Van De Bruaene
  • S. Lucy RocheEmail author
Part of the Congenital Heart Disease in Adolescents and Adults book series (CHDAA)


General cardiologists, emergency room physicians, family doctors and intensivists are all increasingly likely to be faced with an ACHD patient in acute heart failure (HF). Improved awareness of the triggers, pathophysiology and options for management should result in fewer delays, better treatment and improved outcomes. Whilst guidelines exist for the management of chronic HF in ACHD, data and/or guidelines for acute HF are scarce. The ACHD population is heterogeneous and often quite different from patients with acquired heart disease, posing a challenge to the non-specialist and specialist physician alike. This chapter focuses on acute HF in ACHD with illustrative case studies to highlight key messages.


Acute heart failure Subaortic right ventricle Fontan Tetralogy of Fallot Cyanotic congenital heart disease 


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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Peter Munk Cardiac CentreUniversity Health NetworkTorontoCanada
  2. 2.Congenital and Structural CardiologyUniversity Hospitals LeuvenLeuvenBelgium
  3. 3.The Labatt Family Heart CentreThe Hospital for Sick ChildrenTorontoCanada
  4. 4.Division of Cardiology5N-521 Toronto General HospitalTorontoCanada

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