Pathophysiology and Causes of Heart Failure in Adult Congenital Heart Disease

  • Alexandra A. FrogoudakiEmail author
Part of the Congenital Heart Disease in Adolescents and Adults book series (CHDAA)


Congenital heart disease (CHD) predisposes patients to numerous types of heart failure (HF) including systolic and diastolic myocardial dysfunction. There are multiple causes of HF including genetics, arrhythmia, cyanosis, ischemia, and residual hemodynamic lesions. Initial diagnosis, cardiac morphology, and type of surgical repair set the seeds for late-onset heart failure in the adult patient. This chapter will focus on the complex pathophysiology of heart failure in this population and will examine both left and right ventricular disease.


Genetics Fibrosis Myocardial dysfunction Acquired heart disease Arrhythmias 


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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.ATTIKON University Hospital, Athens UniversityAthensGreece

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