Hypoplastic Left Heart Syndrome

  • Monika ChauhanEmail author
  • Susan Tourner
  • Christopher W. Mastropietro


Patients with hypoplastic left heart syndrome (HLHS) are born without a functional left ventricle. To allow for long-term viability, these children typically undergo a series of operations aimed at utilizing the single functional right ventricle to support systemic cardiac output. As a result, these infants are susceptible to unique clinical presentations and require careful management decisions to prevent undesirable outcomes. This chapter focuses on clinical presentation of hypoplastic left heart syndrome at various stages, available surgical options, and common interstage complications that should be familiar to all clinicians who may encounter these children.


Hypoplastic left heart syndrome Heart ventricles Cardiac output 


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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  • Monika Chauhan
    • 1
    Email author
  • Susan Tourner
    • 2
    • 3
  • Christopher W. Mastropietro
    • 4
  1. 1.Division of Critical Care, Department of PediatricsChildren’s Hospital of Michigan, Wayne State University School of MedicineDetroitUSA
  2. 2.Department of PediatricsUniversity of Toledo College of MedicineToledoUSA
  3. 3.ProMedica Toledo Children’s HospitalToledoUSA
  4. 4.Indiana University School of MedicineRiley Hospital for Children at Indiana University HealthIndianapolisUSA

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