Idiopathic Portal Hypertension (Portosinusoidal Disease)

  • Virginia Hernández-Gea
  • Ernest Belmonte
  • Angeles García-Criado
  • Juan Carlos García-Pagán
Chapter

Abstract

Idiopathic portal hypertension is a rare cause of intrahepatic portal hypertension (PH) of uncertain etiology and frequently misdiagnosed. Commonly the diagnosis is made when PH related complications such as ascites and variceal bleeding appear in the absence of cirrhosis, portal vein thrombosis or other specific liver diseases.

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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  • Virginia Hernández-Gea
    • 1
    • 2
  • Ernest Belmonte
    • 3
  • Angeles García-Criado
    • 3
  • Juan Carlos García-Pagán
    • 1
    • 2
  1. 1.Hepatic Hemodynamic Laboratory, Liver Unit, Hospital Clinic, IDIBAPSUniversitat de BarcelonaBarcelonaSpain
  2. 2.Centro de Investigación Biomédica en Red de Enfermedades Hepáticas y Digestivas, CIBERehdInstituto de Salud Carlos IIIMadridSpain
  3. 3.Department of Radiology, Hospital ClinicUniversitat de BarcelonaBarcelonaSpain

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