Ebstein’s Anomaly of the Tricuspid Valve

  • Jonathan Kochav
Part of the In Clinical Practice book series (ICP)


  • Ebstein’s anomaly of the tricuspid valve accounts for less than 1% of all cases of congenital heart disease, occurring in around 0.5 per 10,000 live births. The age at diagnosis can vary widely, from infancy to elder age, based on the wide spectrum of disease severity that exists. This chapter discusses the embryology and anatomy of Ebstein’s anomaly, the structural and electrical defects that are commonly associated with this malformation, and the surgical and electrophysiological management of these patients when they present as adults.


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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  • Jonathan Kochav
    • 1
  1. 1.Massachusetts General HospitalBostonUSA

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