Advertisement

Valvular Pulmonic Stenosis

  • Jonathan Kochav
Chapter
Part of the In Clinical Practice book series (ICP)

Abstract

Valvular pulmonic stenosis is a relatively common congenital lesion occurring in approximately 7% of all patients with congenital heart disease. Isolated PS is the second most common congenital cardiac defect and represents the overwhelming majority (80–90%) of the lesions which cause RV outflow obstruction. This chapter describes the anatomy and physiology of this disease, and the options and indications for surgical or percutaneous intervention in adult patients.

References

  1. 1.
    Reller MD, Strickland MJ, Riehle-Colarusso T, Mahle WT, Correa A. Prevalence of congenital heart defects in metropolitan Atlanta, 1998-2005. J Pediatr. 2008;153:807–13.CrossRefGoogle Scholar
  2. 2.
    Hoffman JI, Christianson R. Congenital heart disease in a cohort of 19,502 births with long-term follow-up. Am J Cardiol. 1978;42:641–7.CrossRefGoogle Scholar
  3. 3.
    DeFaria Yeh D, King ME. Congenital heart disease in the adult: what should the adult cardiologist know? Curr Cardiol Rep. 2015;17:25.CrossRefGoogle Scholar
  4. 4.
    Sellors TH. Surgery of pulmonary stenosis; a case in which the pulmonary valve was successfully divided. Lancet. 1948;1:988.CrossRefGoogle Scholar
  5. 5.
    Kan JS, White RI Jr, Mitchell SE, Gardner TJ. Percutaneous balloon valvuloplasty: a new method for treating congenital pulmonary-valve stenosis. N Engl J Med. 1982;307:540–2.CrossRefGoogle Scholar
  6. 6.
    Warnes CA, Williams RG, Bashore TM, et al. ACC/AHA 2008 guidelines for the management of adults with congenital heart disease: a report of the American College of Cardiology/American Heart Association task force on practice guidelines (writing committee to develop guidelines on the management of adults with congenital heart disease). Circulation. 2008;118:e714–833.PubMedPubMedCentralGoogle Scholar
  7. 7.
    Tami LF, McElderry MW. Pulmonary artery aneurysm due to severe congenital pulmonic stenosis. Case report and literature review. Angiology. 1994;45:383–90.CrossRefGoogle Scholar
  8. 8.
    Altrichter PM, Olson LJ, Edwards WD, Puga FJ, Danielson GK. Surgical pathology of the pulmonary valve: a study of 116 cases spanning 15 years. Mayo Clin Proc. 1989;64:1352–60.CrossRefGoogle Scholar
  9. 9.
    Cuypers JA, Witsenburg M, van der Linde D, Roos-Hesselink JW. Pulmonary stenosis: update on diagnosis and therapeutic options. Heart. 2013;99:339–47.CrossRefGoogle Scholar
  10. 10.
    Sznajer Y, Keren B, Baumann C, et al. The spectrum of cardiac anomalies in Noonan syndrome as a result of mutations in the PTPN11 gene. Pediatrics. 2007;119:e1325–31.CrossRefGoogle Scholar
  11. 11.
    Nora JJ, Nora AH. Recurrence risks in children having one parent with a congenital heart disease. Circulation. 1976;53:701–2.CrossRefGoogle Scholar
  12. 12.
    Khairy P, Marelli AJ. Clinical use of electrocardiography in adults with congenital heart disease. Circulation. 2007;116:2734–46.CrossRefGoogle Scholar
  13. 13.
    Rhodes JF, Hijazi ZM, Sommer RJ. Pathophysiology of congenital heart disease in the adult, part II. Simple obstructive lesions. Circulation. 2008;117:1228–37.CrossRefGoogle Scholar
  14. 14.
    Hayes CJ, Gersony WM, Driscoll DJ, et al. Second natural history study of congenital heart defects. Results of treatment of patients with pulmonary valvar stenosis. Circulation. 1993;87:I28–37.PubMedGoogle Scholar
  15. 15.
    Stanger P, Cassidy SC, Girod DA, Kan JS, Lababidi Z, Shapiro SR. Balloon pulmonary valvuloplasty: results of the Valvuloplasty and Angioplasty of Congenital Anomalies Registry. Am J Cardiol. 1990;65:775–83.CrossRefGoogle Scholar
  16. 16.
    Sadr-Ameli MA, Sheikholeslami F, Firoozi I, Azarnik H. Late results of balloon pulmonary valvuloplasty in adults. Am J Cardiol. 1998;82:398–400.CrossRefGoogle Scholar
  17. 17.
    Teupe CH, Burger W, Schrader R, Zeiher AM. Late (five to nine years) follow-up after balloon dilation of valvular pulmonary stenosis in adults. Am J Cardiol. 1997;80:240–2.CrossRefGoogle Scholar
  18. 18.
    Kanter KR, Budde JM, Parks WJ, et al. One hundred pulmonary valve replacements in children after relief of right ventricular outflow tract obstruction. Ann Thorac Surg. 2002;73:1801–6; discussion 1806–7.CrossRefGoogle Scholar
  19. 19.
    Meadows JJ, Moore PM, Berman DP, et al. Use and performance of the melody transcatheter pulmonary valve in native and postsurgical, nonconduit right ventricular outflow tracts. Circ Cardiovasc Interv. 2014;7:374–80.CrossRefGoogle Scholar
  20. 20.
    O’Connor BK, Beekman RH, Lindauer A, Rocchini A. Intermediate-term outcome after pulmonary balloon valvuloplasty: comparison with a matched surgical control group. J Am Coll Cardiol. 1992;20:169–73.CrossRefGoogle Scholar
  21. 21.
    DeFaria Yeh D, Ghoshhajra B, Inglessis-Azuaje I, MacGillivray T, Liberthson R, Bhatt AB. Massive pulmonary artery aneurysm causing left main coronary artery compression in the absence of pulmonary hypertension. Tex Heart Inst J. 2015;42:465–7.CrossRefGoogle Scholar
  22. 22.
    Canobbio MM, Warnes CA, Aboulhosn J, et al. Management of pregnancy in patients with complex congenital heart disease: a scientific statement for healthcare professionals from the American Heart Association. Circulation. 2017;Google Scholar
  23. 23.
    Oylumlu M, Aykent K, Soydinc HE, et al. Pulmonary balloon valvuloplasty during pregnancy. Case Rep Cardiol. 2012;2012:353168.PubMedPubMedCentralGoogle Scholar

Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  • Jonathan Kochav
    • 1
  1. 1.Massachusetts General HospitalBostonUSA

Personalised recommendations