Anomalous Pulmonary Venous Return

  • Jonathan Kochav
Part of the In Clinical Practice book series (ICP)


The incidence of partial anomalous pulmonary venous return is estimated to be at least 7 per 1000 individuals. The number and size of the anomalous vessels will define the size of the left-to-right shunt, and the severity of presentation can vary from mild disease identified incidentanlly to right-sided volume overload, severe pulmonary hypertension, and right ventricular failure. This chapter covers the anatomy and physiology of the disease, options and indications for surgical repair, and the management of adult survivors. Total anomalous pulmonary venous return is a rare but severe manifestation of anomalous pulmonary venous return generally presenting in infancy, but also receives mention in this chapter.


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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  • Jonathan Kochav
    • 1
  1. 1.Massachusetts General HospitalBostonUSA

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