Primary cutaneous lymphomas (PCL) encompass primary cutaneous B-cell lymphomas (PCBCL) and primary cutaneous T-cell lymphomas (PCTCL). PCL is a heterogeneous group of disorders classified by the WHO-EORTC, and the treatment varies by subtype. General principles regarding work-up and management paradigms are discussed for a subset of these diseases.
KeywordsPrimary cutaneous B-cell lymphoma Primary cutaneous T-cell lymphoma Mycosis fungoides Sézary syndrome
We thank Amy Gillis, Thomas T. Bui, and Mack Roach III for their work on the prior edition of this chapter.
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