Abstract
Neuromyelitis optica spectrum disorders (NMOSD) can present in pediatric patients as isolated optic neuritis. This chapter reviews the case of a 7-year-old girl with sequential vision loss in her left and right eye, respectively, over a 3-month period. Her cerebrospinal fluid tested positive for aquaporin-4 (AQP4)-IgG antibody, and she was diagnosed with NMOSD. Current NMOSD therapies include rituximab, azathioprine, and mycophenolate mofetil. The majority of patients with NMOSD with optic neuritis experience some long-term vision loss.
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Francisco, C., Waubant, E. (2017). Neuromyelitis Optica Presenting with Bilateral Optic Neuritis. In: Waubant, E., Lotze, T. (eds) Pediatric Demyelinating Diseases of the Central Nervous System and Their Mimics. Springer, Cham. https://doi.org/10.1007/978-3-319-61407-6_41
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DOI: https://doi.org/10.1007/978-3-319-61407-6_41
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