Glycogen Storage Diseases
The inherited glycogen storage diseases (GSD) are rare inborn errors of glycogen metabolism. The diseases that survive to adulthood with implications for anesthesia are discussed here. They follow autosomal recessive inheritance. Strategies for medical management that are safe for both mother and fetus will be presented. The anesthetic management of labor and delivery as well as operative deliveries will be discussed.
KeywordsAnesthesia Obstetrical McArdle disease Pompe disease Glycogen storage diseases
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