Factor XIII Deficiency

  • James P. R. BrownEmail author
  • Joanne Douglas


This chapter outlines the pathophysiology, clinical presentation, inheritance, and incidence of factor XIII deficiency. The chapter describes the interaction with pregnancy and discusses the medical and anesthetic management of pregnant women with factor XIII deficiency, including treatment of acute hemorrhage.


Factor XIII deficiency Inherited bleeding disorder Inherited coagulopathy 


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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.UBC Department of Anesthesiology, Pharmacology and TherapeuticsBC Women’s HospitalVancouverCanada
  2. 2.Department of AnesthesiaBC Women’s HospitalVancouverCanada

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