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Pheochromocytoma

  • Emily E. SharpeEmail author
Chapter

Abstract

Pheochromocytomas are catecholamine-secreting tumors that can lead to paroxysmal hypertension. These tumors are rare in pregnancy, but early diagnosis is important for improved maternal and fetal outcomes. Multidisciplinary management is essential and timing of resection depends on the gestational age at diagnosis. Primary goals include avoidance of a hypertensive crisis during delivery and definitive surgical resection. Cesarean delivery is the preferred mode in patients with an unresected pheochromocytoma and can be accomplished safely with general anesthesia, epidural anesthesia, or combined epidural-general anesthesia. The neonate and patient should be monitored closely in the postoperative period.

Keywords

Pheochromocytoma Pregnancy Hypertension Adrenal gland neoplasm Preeclampsia Anesthesia Catecholamines Paraganglioma 

Abbreviations

MEN

Multiple endocrine neoplasia

MRI

Magnetic resonance imaging

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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Department of Anesthesiology and Perioperative MedicineMayo Clinic College of MedicineRochesterUSA

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