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Lymphedema pp 743-752 | Cite as

Primary Lymphedema and Lymphatic Malformation

  • Ningfei LiuEmail author
Chapter
  • 1.6k Downloads

Abstract

Primary lymphedema is defined as edema caused by lymphatic dysplasia or/and dysfunction due to congenital or unknown factors. The clinical manifestations of primary lymphedema are variable. Based on MR lymphangiography, lymphatic system malformations in primary lymphedema can be classified as (1) lymph nodes affected with nodal structural abnormality, (2) lymph vessel affected with hypoplasia/aplasia, (3) both lymph vessel and lymph node affected with subgroups, and (4) lymphatic dysfunction. The classification proposed may be helpful in further studies focused on the development of more appropriate target-oriented treatment.

Keywords

Primary Lymphedema Lymphatic Malformations Lymphatic Dysfunction Yellow Nail Syndrome Chylous Reflux 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer International Publishing AG 2018

Authors and Affiliations

  1. 1.Lymphology Center of Dept. Plastic & Reconstructive Surgery,Shanghai Ninth People’s Hospital, Shanghai Jiao Tong University School of MedicineShanghaiChina

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