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Hemangiopericytoma

  • Vincent Bernard
  • Amol J. Ghia
Chapter

Abstract

Hemangiopericytoma (HPC) is a rare type of mesenchymal tumor associated with an aggressive phenotype with a predilection toward poor local control and subsequent metastasis. As these tumors cannot be readily distinguished from other tumorigenic entities by radiographic imaging alone, a tissue is required to make an effective diagnosis. The ability to make this diagnosis is vital in the context of HPC as this tumor type requires an aggressive therapeutic approach and vigilant follow-up. The current therapeutic strategy for HPC involves maximal safe surgical resection followed by adjuvant radiotherapy. Repeat resection or salvage radiotherapy is also indicated at the time of recurrence or development of metastasis. By maintaining an attentive follow-up schedule for patients with HPC, clinicians may be able to improve patient outcomes.

Keywords

Hemangiopericytoma Solitary fibrous tumor Gamma knife radiosurgery Cyberknife radiosurgery Stereotactic radiotherapy Rare tumors 

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Copyright information

© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Department of PathologyMD Anderson Cancer CenterHoustonUSA
  2. 2.Department of Radiation OncologyMD Anderson Cancer CenterHoustonUSA

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