Anomalies of Kidney Rotation, Position, and Fusion

  • Samuel StafraceEmail author
  • Gabriele Benz-Bohm
Part of the Medical Radiology book series (MEDRAD)


Congenital anomalies of kidney rotation, position, and fusion are very common and are frequently identified by chance. They can be considered as a “normal variant,” as long as they do not cause complications or are related to other problems such as urinary drainage impairment, dysplasia, VUR, infection, or other associated malformations. This chapter describes the embryology, multimodality imaging appearances and complications of this spectrum of pathologies.


  1. Abeshouse BS, Bhisitkul I (1959) Crossed renal ectopia with and without fusion. Urol Int 9:63–91CrossRefPubMedGoogle Scholar
  2. Boatman DL, Kolln CP, Flocks RH (1972) Congenital anomalies associated with horseshoe kidney. J Urol 107:205–207CrossRefPubMedGoogle Scholar
  3. Buntley D (1976) Malignancy associated with horseshoe kidney. Urology 8:146–148CrossRefPubMedGoogle Scholar
  4. Campbell MF (1930) Renal ectopy. J Urol 24:187–198CrossRefGoogle Scholar
  5. Campbell MF (1970) Anomalies of the kidney. In: Campbell MF, Harrison JH (eds) Urology, vol 2, 3rd edn. Saunders, Philadelphia, pp 1416–1486Google Scholar
  6. Chawla A (2013) BMJ case reports. doi: 10.1136/bcr-2013-201163 CrossRefGoogle Scholar
  7. Currarino G, Wood B, Majd M (1993) The genitourinary tract and retroperitoneum. Congenital renal anomalies. In: Silverman FN, Kuhn JP (eds) Caffey’s pediatric X-ray diagnosis: an integrated imaging approach, vol 2, 9th edn. Mosby, St Louis, pp 1223–1243Google Scholar
  8. Dajani AM (1966) Horseshoe kidney: a review of 29 cases. Br J Urol 38:388–402CrossRefPubMedGoogle Scholar
  9. Daneman A, Alton DJ (1991) Radiographic manifestations of renal anomalies. Radiol Clin North Am 29:351–363PubMedGoogle Scholar
  10. Downs RA, Lane JW, Burns E (1973) Solitary pelvic kidney: its clinical implications. Urology 1:51–56CrossRefPubMedGoogle Scholar
  11. Evans WP, Resnick MI (1981) Horseshoe kidney and urolithiasis. J Urol 125:620–621CrossRefPubMedGoogle Scholar
  12. Glenn JF (1959) Analysis of 51 patients with horseshoe kidney. N Engl J Med 261:684–687CrossRefPubMedGoogle Scholar
  13. Kakei H, Kondo A, Ogisu BI, Mitsuya H (1976) Crossed ectopia of solitary kidney: a report of two cases and a review of the literature. Urol Int 31:470–475CrossRefPubMedGoogle Scholar
  14. Kissane JM (1983) Congenital malformations. In: Heptinstall RH (ed) Pathology of the kidney, vol 1, 3rd edn. Little, Brown, Boston, pp 83–140Google Scholar
  15. Kramer SASA, Kelalis PP (1984) Ureteropelvic junction obstruction in children with renal ectopy. J Urol 5:331–336Google Scholar
  16. Lippe B, Geffner ME, Dietrich RB, Boechat MI, Kangarloo H (1988) Renal malformation in patients with Turner’s syndrome: imaging in 141 patients. Pediatrics 82:852–856PubMedGoogle Scholar
  17. Malek RS, Kelalis PP, Burke EC (1971) Ectopic kidney in children and frequency of association with other malformations. Mayo Clin Proc 46:461–467PubMedGoogle Scholar
  18. McDonald JH, McClellan DS (1957) Crossed renal ectopia. Am J Surg 93:995–1002CrossRefPubMedGoogle Scholar
  19. Mesrobian HJ, Kelalis PP, Hrabovsky E, Othersen HB, DeLorimier A, Nesmith B (1985) Wilms’ tumor in horseshoe kidneys: a report from the National Wilms’ Tumor Study. J Urol 133:1002–1003CrossRefPubMedGoogle Scholar
  20. Moore KL, Persaud TVN (1998) The developing human. Clinically oriented embryology, 6th edn. Saunders, PhiladelphiaGoogle Scholar
  21. Muttarak M, Sriburi T (2011) Congenital renal anomalies detected in adulthood. Biomed Imaging Interv J 8(1):e7Google Scholar
  22. N’Guessen G, Stephens FD, Pick J (1984) Congenital superior ectopic (thoracic) kidney. Urology 24:219–228CrossRefPubMedGoogle Scholar
  23. Pitts WR Jr, Muecke EC (1975) Horseshoe kidneys: a 40-year experience. J Urol 113:743–746CrossRefPubMedGoogle Scholar
  24. Polak-Jonkisz D, Fornalczyk K, Musial K et al (2012) Crossed renal ectopia: can it be a diagnostic problem? Postepy Hig Med Dosw 66:201–214CrossRefGoogle Scholar
  25. Ritchey M (1992) Anomalies of the kidney. In: Kelalis PP, King LR, Belman AB (eds) Clinical pediatric urology, vol 1, 3rd edn. Saunders, Philadelphia, pp 500–528Google Scholar
  26. Rubinstein ZJ, Hertz M, Shahin N, Deutsch V (1976) Crossed renal ectopia: angiographic findings in six cases. Am J Roentgenol 126:1035–1038CrossRefGoogle Scholar
  27. Thompson GJ, Pace JM (1937) Ectopic kidney: a review of 97 cases. Surg Gynecol Obstet 64:935–943Google Scholar
  28. Warkany J, Passarge E, Smith LB (1966) Congenital malformations in autosomal trisomy syndromes. Am J Dis Child 112:502–517PubMedGoogle Scholar
  29. Whitaker RH, Hunt GM (1987) Incidence and distribution of renal anomalies in patients with neural tube defects. Eur Urol 13:322–323CrossRefPubMedGoogle Scholar
  30. Zondek LH, Zondek T (1964) Horseshoe kidney in associated congenital malformations. Urol Int 18:347–356CrossRefPubMedGoogle Scholar

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© Springer International Publishing AG, part of Springer Nature 2018

Authors and Affiliations

  1. 1.Sidra Medical and Research CenterDohaQatar
  2. 2.Department of RadiologyThe Children’s Hospital of PhiladelphiaPhiladelphiaUSA

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