Tetralogy of Fallot: Management of the Pulmonary Valve

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Abstract

Repair of TOF can be accomplished with low mortality and excellent long-term survival. Event free survival however remains a significant problem. Long-term procedural risks related to right ventricular outflow tract obstruction or more importantly right ventricular dilatation, dysfunction and arrhythmia related to chronic pulmonary insufficiency, continue to affect our patients. Adequate relief of right ventricular outflow tract obstruction with emphasis on preserving a functional right ventricle as well as valve preservation strategies at the time of surgical repair, are recommended. A precise evaluation of the anatomy and technical readiness to perform valve-preserving procedures are essential for the surgeon. Inferences from long term data out to 50 years support these concepts.

Keywords

Tetralogy of Fallot Pulmonary valve morphology Pulmonary valve sparing surgery Pulmonary regurgitation 
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Copyright information

© Springer International Publishing Switzerland 2016

Authors and Affiliations

  1. 1.Division of Cardiac Surgery, Department of Cardiovascular SurgeryJohns Hopkins All Children’s Heart Institute, All Children’s HospitalSt. PetersburgUSA

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