Anatomic diagnosis pre-main repair: The repair of anorectal malformation should not be a surgical exploration or a surgical misadventure. It is supposed to be a well-planned procedure based on an accurate anatomic diagnosis. In order to achieve that, it is important to perform technically correct imaging procedures. The “high-pressure distal colostogram” is the most valuable and important diagnostic study in the management of anorectal malformations. A detailed description of this procedure with adequate images as well as an animation will illustrate this extremely important diagnostic test.

In this chapter, the authors also describe the value of ultrasound studies of the female pelvic anatomy during the neonatal period. The value of the MRI studies, particularly in patients already operated, is discussed, and special space is dedicated to describe an extremely valuable, modern imaging procedure called “3D rotational scan” that is extremely helpful in the management of complex cloacal malformations.


Anorectal Malformation Transverse Colostomy Urinary Control Sphincter Mechanism Perineal Fistula 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

Supplementary material

Animation 6.1

Muscle action (WMV 6049 kb)

Animation 6.2

Distal colostogram in a case of rectourethral bulbar fistula (WMV 10656 kb)

Animation 6.3

Distal colostogram in a case of rectourethral prostatic fistula (WMV 17857 kb)

Animation 6.4

Distal colostogram in a case of recto-bladder neck fistula (WMV 11617 kb)

Animation 6.5

Posterior urethral diverticulum in a patient with a rectourethral-bulbar fistula, approached laparoscopically (WMV 19552 kb)

328507_1_En_6_MOESM6_ESM.gif (40.4 mb)
Video 6.1 (GIF 41350 kb)
328507_1_En_6_MOESM7_ESM.gif (7.2 mb)
Video 6.2 (GIF 7337 kb)
328507_1_En_6_MOESM8_ESM.avi (362.1 mb)
Video 6.3 (AVI 370799 kb)


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Copyright information

© Springer International Publishing Switzerland 2015

Authors and Affiliations

  • Alberto Peña
    • 1
  • Andrea Bischoff
    • 1
  1. 1.Pediatric SurgeryColorectal Center for Children Cincinnati Children’s HospitalCincinnatiUSA

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