Ebstein’s Anomaly with Severe Tricuspid Regurgitation, Severe Septal Displacement Ratio, and Grade 3 Right Atrial Cavity Ratio
A young man presented with a history of frequent episodes of palpitation and exercise intolerance of 3-month duration. Physical examination showed a blood pressure of 130/80 mmHg, regular pulse rate of 85 beats per minute, normal jugular venous pressure, widely split S1 with a loud tricuspid component (sail sound), right-sided third heart sound, and pansystolic murmur, which increased with inspiration and could be best heard at the lower left sternal border. The body surface area was equal to 1.7 m2. The patient was a candidate for the radiofrequency ablation of paroxysmal supraventricular tachycardia. Transthoracic echocardiography showed a normal left ventricular size with mild systolic dysfunction and a left ventricular ejection fraction of about 45 %. The right ventricular systolic function, in terms of the fractional area change (FAC), was normal (FAC = 66 %).
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