Supravalvular Aortic Stenosis – Hourglass Type

  • Hakimeh Sadeghian
  • Zahra Savand-Roomi


A young man with a history of palpitation and two episodes of syncopal attacks and a systolic murmur (grade IV/VI) in the aortic area was referred to our echocardiography laboratory for an evaluation of the cardiac cause of the syncopal attacks. Echocardiography revealed normal left and right ventricular sizes and systolic functions as well as concentric left ventricular hypertrophy.

Supplementary material

Video 104.1

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  1. 2.
    Webb GD, Smallhorn J, Therrien J, Redington AN. Congenital heart disease. In: Bonow RO, Mann D, Zipes DP, Libby P, Breunwald E, editors. Braunwald heart disease, a text book of cardiovascular medicine. 9th ed. Philadelphia: Elsevier Saunders; 2012. p. 1411–67.Google Scholar
  2. 87.
    Lopez L. Abnormalities of left ventricular outflow. In: Eidem BW, Cetta F, O’Leary PW, editors. Echocardiography in pediatric and adult congenital heart disease. Philadelphia: Lippincott Williams and Wilkins; 2010. p. 215–36.Google Scholar
  3. 118.
    Schneider DJ, Moore J. Aortic stenosis. In: Allen HA, Driscoll D, Shaddy RE, Feltes TF, editors. Moss and Adams’ heart disease in infants, children, and adolescents. 8th ed. Philadelphia: Lippincott Williams & Wilkins; 2013. p. 1023–43.Google Scholar
  4. 119.
    Neutze JM, Calder A, Gentles TL, Wilson NJ. Aortic stenosis. In: Moller JH, Hoffman JIE, editors. Pediatric cardiovascular medicine. 1st ed. Philadelphia: Churchill Livingstone; 2000. p. 511–51.Google Scholar

Copyright information

© Springer International Publishing Switzerland 2015

Authors and Affiliations

  • Hakimeh Sadeghian
    • 1
  • Zahra Savand-Roomi
    • 2
  1. 1.Department of EchocardiographyTehran University of Medical Sciences Tehran Heart CentreTehranIran
  2. 2.Department of EchocardiographyKowsar HospitalShirazIran

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