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Arrhythmogenic Right Ventricular Cardiomyopathy: Clinical Assessment and Differential Diagnosis

  • Francesca BrunEmail author
  • Concetta Di Nora
  • Marco Merlo
  • Alberto Pivetta
  • Luisa Mestroni
  • Gianfranco Sinagra
Chapter

Abstract

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is an inherited cardiovascular disorder leading to life-threatening ventricular arrhythmias, progressive biventricular dysfunction, and heart failure. Sudden death can be the unique feature of the disease. Genetic studies indicate that ARVC should be considered a disease of desmosome dysfunction. Diagnosis remains a clinical challenge mainly in its early stages and in patients with minimal imaging structural abnormalities. ARVC shares some common features with other cardiac diseases, such as RV outflow tract ventricular tachycardia, Brugada syndrome, dilated cardiomyopathy, and myocarditis, due to arrhythmic expressivity and biventricular involvement. Diagnosis is based on major and minor criteria listed in the Revised Task Force Criteria.

Keywords

Cardiac Magnetic Resonance Late Gadolinium Enhancement Arrhythmogenic Right Ventricular Cardiomyopathy Brugada Syndrome Task Force Criterion 
These keywords were added by machine and not by the authors. This process is experimental and the keywords may be updated as the learning algorithm improves.

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Copyright information

© Springer International Publishing Switzerland 2014

Authors and Affiliations

  • Francesca Brun
    • 1
    Email author
  • Concetta Di Nora
    • 1
  • Marco Merlo
    • 1
  • Alberto Pivetta
    • 1
  • Luisa Mestroni
    • 2
  • Gianfranco Sinagra
    • 1
  1. 1.Department of CardiologyUniversity Hospital of TriesteTriesteItaly
  2. 2.Department of Molecular Genetics, Cardiovascular InstituteUniversity of Colorado Denver Anschutz Medical CampusAuroraUSA

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