The General Approach to Cystic Fibrosis Pulmonary Infection in The Netherlands
Summary
In the Netherlands, a national registry provides patient data on the demography of cystic fibrosis (CF). The survival rate of patients with CF has increased considerably over the last decade. The improved survival rate is in part attributable to management and care of these patients by multidisciplinary treatment in CF centres. Early diagnosis of CF, preferably made at the neonatal stage, will lead to improved patient treatment in order to delay deterioration in lung function. Treatment involves a comprehensive approach based on intensive antiobiotic therapy and physiotherapy in addition to nutritional and psychosocial support. Improvement of selective culture media has resulted in enhanced recovery of bacterial pathogens in CF, resulting in better basis for a rational choice of the antibiotic regimen. The complex pathogenic bacterial flora usually requires a combined therapeutic antibiotic treatment, especially for Pseudomonoas aeruginosa infections. The cornerstone of pulmonary care in CF is prevention of pulmonary deterioration through physiotherapy in combination with prophylactic antimicrobial therapy, an optimal nutritional state and possibly vaccination.
Keywords
Cystic Fibrosis Cystic Fibrosis Patient Fusidic Acid Penicillin Allergy Chest PhysiotherapyPreview
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