Cystic Fibrosis

  • Adrienne P. Borschuk
  • Stephanie S. FilignoEmail author
Part of the Issues in Clinical Child Psychology book series (ICCP)


Cystic fibrosis (CF) is a life-shortening genetic disease that results in the overproduction of thick, sticky mucus throughout the body. Symptoms are progressive, and management requires a burdensome daily medical regimen. Individuals with CF also require hospital admissions lasting 10–14 days to treat illness exacerbations. Given that individuals with CF and their caregivers are more likely to develop symptoms of anxiety and depression, inpatient CL providers are in a prime position to deliver psychological treatment to children and families while also interfacing with and educating the medical team (both inpatient and outpatient). Common referral concerns can include, but are not limited to, anxiety and depression, adherence promotion, coping with disease progression, and promoting function in the hospital environment. Working effectively with bedside staff and attending medical providers are a key focus of treatment for individuals with CF and their families. Aspects of interventions should be modified as appropriate for this population, particularly keeping in mind infection control guidelines.


CF exacerbation Hospital coping Procedural anxiety Interdisciplinary communication Adherence promotion Psychotherapy 


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Copyright information

© Springer Nature Switzerland AG 2020

Authors and Affiliations

  • Adrienne P. Borschuk
    • 1
    • 2
    • 3
  • Stephanie S. Filigno
    • 1
    • 2
    • 3
    Email author
  1. 1.Cincinnati Children’s Hospital Medical CenterCincinnatiUSA
  2. 2.Behavioral Medicine and Clinical PsychologyCincinnati Children’s Hospital Medical CenterCincinnatiUSA
  3. 3.University of Cincinnati College of MedicineCincinnatiUSA

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