Coronary Artery Abnormalities in Patients with Kawasaki Disease and Williams Syndrome

  • Randy Ray Richardson


The most common and serious complications of Kawasaki disease are coronary artery abnormalities. In patients with Kawasaki disease, coronary artery involvement is seen in approximately 15–20% of patients [1]. Over the years, the definition of coronary artery involvement has varied but it is now defined by internal lumen diameter, adjusted to body surface area Z-scores [2–4]. Table 8.1 depicts the current classification system for coronary artery abnormalities seen in patients with Kawasaki disease [2–4].


Kawasaki disease Coronary artery aneurysms Williams syndrome Coronary artery stenosis 


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© Springer Nature Switzerland AG 2020

Authors and Affiliations

  • Randy Ray Richardson
    • 1
  1. 1.Creighton University School of Medicine, St. Joseph’s Hospital and Medical CenterPhoenixUSA

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