Coronary Artery Abnormalities in Patients with Kawasaki Disease and Williams Syndrome
The most common and serious complications of Kawasaki disease are coronary artery abnormalities. In patients with Kawasaki disease, coronary artery involvement is seen in approximately 15–20% of patients . Over the years, the definition of coronary artery involvement has varied but it is now defined by internal lumen diameter, adjusted to body surface area Z-scores [2–4]. Table 8.1 depicts the current classification system for coronary artery abnormalities seen in patients with Kawasaki disease [2–4].
KeywordsKawasaki disease Coronary artery aneurysms Williams syndrome Coronary artery stenosis
- 6.Orenstein JM, Shulman ST, Fox LM, Baker SC, Takahashi M, Bhatti TR, et al. Three linked vasculo-pathic processes characterize Kawasaki disease: a light and trans- mission electron microscopic study. PLoS One. 2012;7:e38998. https://doi.org/10.1371/journal.pone.0038998.CrossRefPubMedPubMedCentralGoogle Scholar