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Coronary Artery Abnormalities in Patients with Kawasaki Disease and Williams Syndrome

  • Randy Ray Richardson
Chapter

Abstract

The most common and serious complications of Kawasaki disease are coronary artery abnormalities. In patients with Kawasaki disease, coronary artery involvement is seen in approximately 15–20% of patients [1]. Over the years, the definition of coronary artery involvement has varied but it is now defined by internal lumen diameter, adjusted to body surface area Z-scores [2–4]. Table 8.1 depicts the current classification system for coronary artery abnormalities seen in patients with Kawasaki disease [2–4].

Keywords

Kawasaki disease Coronary artery aneurysms Williams syndrome Coronary artery stenosis 

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Copyright information

© Springer Nature Switzerland AG 2020

Authors and Affiliations

  • Randy Ray Richardson
    • 1
  1. 1.Creighton University School of Medicine, St. Joseph’s Hospital and Medical CenterPhoenixUSA

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