Neuromuscular Patients (Amyotrophic Lateral Sclerosis and Other Conditions)
Many progressive neuromuscular disorders involve muscles of the respiratory system which are involved in breathing and coughing. Ventilatory assistance becomes an important part of management for patients with advanced neuromuscular disease. The combination of NIV with cough-assist techniques decreases pulmonary morbidity and hospital admissions.
Technological advancements in NIV have led to a significant improvement in ability to treatment these patients.
Amyotrophic lateral sclerosis
Chronic obstructive pulmonary disease
Myotonic dystrophy type 1
Duchenne muscular dystrophy
Non-invasive positive pressure ventilation
Obstructive sleep apnoea syndrome
Positive end-expiratory pressure
Pressure support ventilation
Quality of life
Sleep disorder breathing
Spinal muscular atrophy
- 10.Lacombe M, Del Amo Castrillo L, et al. Comparison of three cough-augmentation techniques in neuromuscular patients: mechanical insufflation combined with manually assisted cough, insufflation-exsufflation alone and insufflation-exsufflation combined with manually assisted cough. Respiration. 2014;88(3):215–22.CrossRefGoogle Scholar