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Multiple Circinate, Sterile, Flaccid, Relapsing Pustules

  • Selcen Kundak
  • Malik Ergin
Chapter

Abstract

  • Subcorneal pustular dermatosis (SPD), also known as Sneddon-Wilkinson disease, is a rare chronic and recurring flaccid sterile pustular eruption

  • SPD is classified within the “neutrophilic dermatoses” and develops mainly in middle-aged women

  • SPD has been associated with benign IgA gammopathy or IgA elevation without gammopathy, monoclonal gammopathy, pyoderma gangrenosum, rheumatoid arthritis, systemic lupus erythematosus, inflammatory bowel diseases, hyperthyroidism, and apudoma

  • Systemic or topical steroids are used as monotherapy or in combination with dapsone, are first choice treatments for SPD

Keywords

Subcorneal pustular dermatosis IgA gammopathy Steroids Dapsone 

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Copyright information

© Springer Nature Switzerland AG 2020

Authors and Affiliations

  • Selcen Kundak
    • 1
  • Malik Ergin
    • 2
  1. 1.Department of DermatologyDr. Behçet Uz Children’s HospitalİzmirTurkey
  2. 2.Department of PathologyDr. Behçet Uz Children’s HospitalİzmirTurkey

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