Outbreaks of Erythematous and Necrotic Papules with Hemorrhagic Crusts

  • Selcen Kundak
  • Malik Ergin


  • Pityriasis lichenoides (PL) which is also called Mucha-Habermann disease is an uncommon type of self-limited lymphocytic inflammatory dermatosis

  • Pityriasis lichenoides et varioliformis acuta (PLEVA) is one form of PL, presenting with erythematous macules and polymorphic lesions of papules which rapidly evolve into vesicopustular lesions with hemorrhagic and adherent crusts

  • Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a rare and severe variant of PLEVA, characterized by aggressive ulceronecrotic skin lesions, high fever and histologically described by features which are typical of PLEVA

  • Erythromycin and tetracyclines are indicated for their anti-inflammatory effects rather than antibiotic effects in treatment of PLEVA

  • In severe PLEVA or FUMHD, immunosuppressive agents may prove to be successful


Pityriasis lichenoides Pityriasis lichenoides et varioliformis acuta Febrile ulceronecrotic Mucha-Habermann disease Erythromycin Tetracycline 


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Copyright information

© Springer Nature Switzerland AG 2020

Authors and Affiliations

  • Selcen Kundak
    • 1
  • Malik Ergin
    • 2
  1. 1.Department of DermatologyDr. Behçet Uz Children’s HospitalIzmirTurkey
  2. 2.Department of PathologyDr. Behçet Uz Children’s HospitalİzmirTurkey

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