Double Outlet Right Ventricle

  • Ravi S. Samraj
  • Ross M. Ungerleider
  • Inder MehtaEmail author


Double outlet right ventricle (DORV) is a relatively rare group of cardiac anomalies characterized by both great arteries (pulmonary and aorta) arising primarily from the right ventricle. It includes a broad spectrum of anatomical variants and associated malformations. The multiple anatomic variations of this lesion are commonly classified by the relationship of the great vessels to one another and/or by the location of the ventricular septal defect to the great vessels. The location of the ventricular septal defect and its size are critical to the repair. Surgical options include one-stage biventricular repair, biventricular repair with a conduit, or staged palliative single-ventricle surgery. Surgical treatment can be offered to most patients with low operative mortality and excellent long-term survival.


Double outlet right ventricle Heterotaxy syndromes Rastelli procedure Ventriculoarterial connection Ventricular septal defect 


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Copyright information

© Springer Nature Switzerland AG 2020

Authors and Affiliations

  • Ravi S. Samraj
    • 1
  • Ross M. Ungerleider
    • 2
  • Inder Mehta
    • 2
    Email author
  1. 1.Department of Anesthesiology and Pediatric Critical CareUTMB, Driscoll Children’s HospitalCorpus ChristiUSA
  2. 2.Department of Cardiothoracic SurgeryDriscoll Children’s HospitalCorpus ChristiUSA

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